"ସ୍ୱଳ୍ପ ବିକଶିତ ବାମ ହୃତ୍‌ପିଣ୍ଡ ସିଣ୍ଡ୍ରୋମ" ପୃଷ୍ଠାର ସଂସ୍କରଣ‌ଗୁଡ଼ିକ ମଧ୍ୟରେ ତଫାତ

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୩ କ ଧାଡ଼ି:
| risks =
| frequency = 1 in 5,000 newborns<ref name=Stat2020>{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref>
| prognosis = High risk of disability or death<ref name=Stat2020>{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref>
| medication =
| treatment = [[Prostaglandin E1]], surgery, [[palliative care|comfort care]]<ref name=Stat2020>{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref>
| prevention =
| differential = [[Coarctation of the aorta]], [[aortic stenosis]], [[Shone's syndrome]]<ref name=Stat2020>{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref>
| diagnosis = [[Ultrasound]]<ref name=Stat2020>{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref>
| causes = Usually unknown<ref name=CDC2020>{{cite web |title=Congenital Heart Defects - Facts about Hypoplastic Left Heart Syndrome |url=https://www.cdc.gov/ncbddd/heartdefects/hlhs.html |website=Centers for Disease Control and Prevention |access-date=6 February 2021 |language=en-us |date=19 November 2019}}</ref>
| synonym = Cyanotic heart disease - hypoplastic left heart<ref>{{cite web |title=Hypoplastic left heart syndrome: MedlinePlus Medical Encyclopedia |url=https://medlineplus.gov/ency/article/001106.htm |website=medlineplus.gov |accessdate=28 May 2019 |language=en}}</ref>
| types =
| duration =
| onset = [[Birth defect|Present at birth]]<ref name=Stat2020>{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref>
| symptoms = [[Shortness of breath]], [[cyanosis|bluish skin]]<ref name=CDC2020>{{cite web |title=Congenital Heart Defects - Facts about Hypoplastic Left Heart Syndrome |url=https://www.cdc.gov/ncbddd/heartdefects/hlhs.html |website=Centers for Disease Control and Prevention |access-date=6 February 2021 |language=en-us |date=19 November 2019}}</ref>
| specialty = [[Cardiac surgery]]
| pronounce =
୨୧ କ ଧାଡ଼ି:
| deaths =
}}
'''ସ୍ୱଳ୍ପ ବିକଶିତ ବାମ ହୃତ୍‌ପିଣ୍ଡ ସିଣ୍ଡ୍ରୋମ''' ('''Hypoplastic left heart syndrome/''' '''HLHS''' ) ଏକ [[ଜନ୍ମଗତ ହୃତ୍‌ପିଣ୍ଡ ତୃଟି|ଜନ୍ମଗତ ହୃତ୍‌ପିଣ୍ଡ ତ୍ରୁଟି]] ରୋଗ ଯେଉଁଥିରେ ହୃତ୍‌ପିଣ୍ଡର ବାମ ପାର୍ଶ୍ୱ ଗୁରୁତର ଭାବରେ ବିକଶିତ ହୋଇନଥାଏ | <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref> ଏହି ରୋଗରେ ବାମ ନିଳୟ, ଆଓର୍ଟା, ଆଓର୍ଟା ଭଲଭ ଓ ମାଇଟ୍ରାଲ ଭଲଭ ପ୍ରଭାବିତ ହୋଇଥାଏ । <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref> ଜୀବନର ପ୍ରଥମ କିଛି ଦିନ ଶିଶୁଟି ସ୍ୱାଭାବିକ ଦେଖାଯାଏ, କିନ୍ତୁ ପରେ ସେମାନଙ୍କର ଶୀଘ୍ର ନିଶ୍ୱାସ ନେବାରେ ଅସୁବିଧା ସୃଷ୍ଟି ହୁଏ | <ref name="CDC2020">{{cite web |title=Congenital Heart Defects - Facts about Hypoplastic Left Heart Syndrome |url=https://www.cdc.gov/ncbddd/heartdefects/hlhs.html |website=Centers for Disease Control and Prevention |access-date=6 February 2021 |language=en-us |date=19 November 2019}}</ref> ଅନ୍ୟାନ୍ୟ ଲକ୍ଷଣ ମଧ୍ୟରେ ନୀଳ ଚର୍ମ ସ‌ହିତ [[ଅମ୍ଳଜାନ ସାନ୍ଦ୍ରତା]] ୭୫ରୁ ୮୫% ରହେ । <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref>
 
ଏହାର କାରଣ ସାଧାରଣତଃ ଜଣା ପଡିନାହିଁ | <ref name="CDC2020">{{cite web |title=Congenital Heart Defects - Facts about Hypoplastic Left Heart Syndrome |url=https://www.cdc.gov/ncbddd/heartdefects/hlhs.html |website=Centers for Disease Control and Prevention |access-date=6 February 2021 |language=en-us |date=19 November 2019}}</ref> ଏହା [[ଟର୍ନର ସିଣ୍ଡ୍ରୋମ|ଟର୍ନର]], [[ଡାଇଜର୍ଜ ସିଣ୍ଡ୍ରୋମ]], ଏବଂ [[ଡାଉନ ସିଣ୍ଡ୍ରୋମ]] ଭଳି ଅନେକ ଜେନେଟିକ ରୋଗ ସହିତ ଜଡିତ ଥାଏ | <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref> ପ୍ରସବପୁର୍ବ ଅଲଟ୍ରାସାଉଣ୍ଡଦ୍ୱାରା ସାଧାରଣତଃ ଏହି ରୋଗ ନିର୍ଣ୍ଣୟ କରାଯାଏ | <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref>
 
ପ୍ରାରମ୍ଭିକ ଚିକିତ୍ସାରେ ଆରାମ ଦାୟକ ଯତ୍ନ ବା [[ପ୍ରୋସ୍ଟାଗ୍ଲାଣ୍ଡିନ ଇ୧|ପ୍ରୋଷ୍ଟାଗ୍ଲାଡିନ ଇ୧]] ଦିଆଯାଏ | <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref> ଆନ୍ତନିଳୟ ପରଦା ବା ସେପ୍ଟମରେ ଏକ ଛିଦ୍ର କରିବା ଆବଶ୍ୟକ ପଡ଼ିପାରେ । <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref> ଏହା ତିନୋଟି ଅସ୍ତ୍ରୋପଚାରରଦ୍ୱାରା ଅନୁସରଣ କରାଯାଇପାରେ | <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref> ଅସ୍ତ୍ରୋପଚାର ପର୍ଯ୍ୟନ୍ତ ଶିଶୁକୁ ରକ୍ଷା କରିବା ପାଇଁ ଏସିଏମଓ ବ୍ୟବ‌ହାର କରାଯାଏ । <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref> ଚିକିତ୍ସା ବିନା ପିଲାମାନେ ଜୀବନର ପ୍ରଥମ ସପ୍ତାହ ମଧ୍ୟରେ ମରିଯାଆନ୍ତି | <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref> ଚିକିତ୍ସା ସହିତ ପ୍ରାୟ ୬୬% ପିଲା ଅତି କମରେ ୫ ବର୍ଷ ବୟସ ପର୍ଯ୍ୟନ୍ତ ବଞ୍ଚନ୍ତି। <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref>
 
ଏହା ଏକ ବିରଳ ରୋଗ ଅଟେ ଓ ୫,୦୦୦ ନବଜାତଙ୍କ ମଧ୍ୟରୁ ଜଣକର ଏହି ରୋଗ ଥାଏ | <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref> ଜନ୍ମଗତ ହୃଦ୍ ରୋଗରେ ଏହାର ସଂଖ୍ୟା ପ୍ରାୟ ୩% ହୋଇଥାଏ। <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref> ଏହା ପ୍ରଥମେ ୧୯୫୨ ମସିହାରେ ଲେଭ୍ ବର୍ଣ୍ଣନା କରିଥିଲେ | <ref name="Ry2003">{{Cite book|url=https://books.google.ca/books?id=IGG3jbMrwMAC&pg=PA39|title=Hypoplastic Left Heart Syndrome|last=Rychik|first=Jack|last2=Wernovsky|first2=Gil|date=2003|publisher=Springer Science & Business Media|isbn=978-1-4020-7319-9|page=39|language=en}}</ref> ଜନ୍ମ ପୂର୍ବରୁ ଏହି ରୋଗ ନିର୍ଣ୍ଣୟ ହେଲେ ୧୨%ରୁ ୪୮% ପିତାମାତା [[ଗର୍ଭପାତ]] ନିମନ୍ତେ ସମ୍ମତି ପ୍ରଦାନ କରନ୍ତି । <ref name="Stat2020">{{cite journal |last1=Kritzmire |first1=SM |last2=Cossu |first2=AE |title=Hypoplastic Left Heart Syndrome |date=January 2020 |pmid=32119463}}</ref>
 
 
୩୩ କ ଧାଡ଼ି:
<references />
[[ଶ୍ରେଣୀ:ଚିକିତ୍ସା ବିଜ୍ଞାନ]]
[[Category:Translated from MDWiki]]